Table 3: Patient Presentation – Inclusion Criteria According to Benhamou Present in Each Case

Case Inclusion Features – Any one of these 4 Items is Sufficient to Diagnose the Syndrome, in the Absence of an Exclusion Feature.
Skin Manifestations of Severe Acne Skin Manifestations of PPP Hyperostosis with or without Dermatosis CRMO Involving Axial or Peripheral Skeleton, with or without Dermatosis
1 No No Yes Yes
2 No Yes Yes Yes
3 Yes No Yes Yes
4 No Yes Yes Yes
5 No No Yes Yes

PPP = Palmoplantar pustulosis.
CRMO = Chronic Recurrent Multifocal Osteomyelitis.