Table 1: Case Reports of Acute Respiratory Distress Syndrome associated with Adult-Onset Still's Disease

Name Age Sex Fever WBC  (x109/L) %  neut Hb  (g/dL) Plts  (x109/L) CRP  (mg/L) ESR Ferritin  (ng/mL) Therapy Med Hx Other  Symptoms Outcome Time to
Improvement  After
Initiation  of Therapy
Time  Until  Initiation 
of  Steroid
Biron
(2006)
39 F + 22 90 8.4 571 290 * 8590 CS none sore throat,
arthralgia,
skin rash
improved 2 days *
Biron
(2006)
68 F + 28 88 12.1 220 362 116 42600 CS polio, DM dyspnea
arthralgia, rash
improved 3 days *
Biron
(2006)
43 M + 15.6 91 * * 471 * 25195 CS+IVIG none repiratory
distress,
sore throat
improved 2 days *
Chvojka
(2009)
24 M + * * * * * * * CS none sore throat,
rash,
pleural effusion
died * *
Gibbs
(1993)
21 F + * * * * * * * CS none arthralgia,
liver damage,
DIC
improved * *
Guignard
(2007)
23 M + 21 * * * 118 83 >10,000 CS+MTX none sore throat,
rash, arthritis
improved 6 days *
Hagiyama
(2003)
24 F + 12.9 95 11.9 271 26.9 98 103 CS+CYP none liver
damage, DIC
improved 6 days 8 days
Hagiyama
(2003)
20 M + 12.2 88 13.6 170 16.4 * 14455 CS none rash,
 adenopathy
improved 7 days 5 days
Hirohata
(1986)
65 F + 14 * * * * * 7880 CS+CYP none arthralgia,
dyspnea
died died day 37 5 days
Iglesias
(1999)
29 F + 16.6 * 10.1 142 * >100 2600 CS none hypotension,
sore throat
arthralgia
improved 24 hours 6 days
Manganelli
(2003)
17 F + * * * * * 26 * CS +6MP+CSA+IVIG none fever, myalgias,
skin rash,
 dyspnea
died improved
day 20,
died day 31
*
Mito
(2002)
24 F + * * * * * * * CS+CSA none sore throat,
rash, arthritis,
adenopathy
improved * *
Pederson
(1991)
40 M + 33 * * * * 114 * CS+AZA none arthralgia,
jaundice, rash
improved * 9 days
Shinohara
(1999)
54 F + 17.7 84 12.3 370 11.9 92 3801 CS none rash,
polyarthralgia,
myalgia, DIC
improved * *
Suleiman
(2002)
36 F + 30.9 * 10.1 260 * 55 7880 CS +MTX none pleural effusion,
dyspnea
improved less than
1 week
*
Yokoyama
(1995)
71 M + * * * 69 * * 37000 CS+NM none sore throat,
rash, myalgia
improved 24 hours 5 days
Our Case
(2010)
26 F + 20 92 10 407 7.1 39 4022 CS dm sore throat,
myalgias
died 2 days 13 days

* Data/values not reported or unavailable.
Abbreviations: F= female, M=male, WBC = white blood cell count, neut= neutrophil, Plts= Platelets, CRP= C reactive protein, gly= glycosolated, Med = medical, Hx= history, CP = Chest pain, SOB= shortness of breath.
DIC = disseminated intravascular coagulation, DM = diabetes mellitus, CS = corticosteroids, CSA = cyclosporine, CYP = cyclophosphamide, IVIG = intravenous immunoglobulin, MTX = methotrexate, AZA = azathioprine.
6-MP = 6 mercaptopurine, NM=nafamostat mesilate.
Key for Table 1: Abbreviations: F= female, M=male, WBC = white blood cell count, neut= neutrophil, Plts= Platelets, CRP= C reactive protein, gly= glycosolated, Med = medical, Hx= history, CP = Chest pain, SOB= shortness of breath, DIC = disseminated intravascular coagulation, DM = diabetes mellitus, CS = corticosteroids, CSA = cyclosporine, CYP = cyclophosphamide, IVIG = intravenous immunoglobulin, MTX = methotrexate, AZA = azathioprine, 6-MP = 6 mercaptopurine, NM = nafamostat mesilate.